The experience of organizing medical care for children with lipid metabolism disorders on the example of the work of the Lipidology Center of the Children's Republican Clinical Hospital in the Republic of Tatarstan

Abstract

Goal. Increasing the availability of highly qualified pediatric cardiac care for patients with lipid metabolism disorders, improving the diagnosis and effectiveness of treatment of patients with cardiovascular diseases.
Materials and methods. The Lipidology Center for Children was opened on a functional basis on the basis of the Children's Republican Clinical Hospital of the Republic of Tatarstan (DRKB MH RT) in 2018. The center's tasks include identifying, treating and monitoring patients with complex disorders of lipid metabolism (including hereditary forms), maintaining the federal register of familial hypercholesterolemia (FHC) and other rare disorders of lipid metabolism; training of doctors and patients. The scheme of cascade screening operation in the framework of interaction between adult and pediatric lipidology centers has been demonstrated.
Results. When conducting cascade screening at the Center for Lipidology for Children, DRKB MH RT in cooperation with the Center for Lipidology for Adults at the City Clinical Hospital No. 7 (GKB No. 7) in Kazan, 203 patients aged 0 to 17 years with a burdened family history were identified on cardiovascular diseases. Upon further examination, 84 children showed an increase in total cholesterol and / or LDL levels above the reference values. Familial hypercholesterolemia was diagnosed in 34 patients, which accounted for 16.8% of all examined patients. Cascade screening provides active detection of patients with lipid metabolism disorders, both children and adults.
Conclusion. The Lipidology Center for Children allows not only to carry out medical and preventive work, but also to ensure the coordinated interaction of various structural units of health care in the fight against atherosclerosis in children and adults. Based on the experience of the Center, it can be argued that the introduction of such units in the structure of medical institutions on the territory of the Russian Federation allows for the effective organization of diagnostics, treatment and prevention of patients with lipid metabolism disorders, has obvious clinical benefits.